It accounts for 5-8% of childhood cancers. The commonest site of involvement
is head and neck. It occurs with increased frequency in patients with neurofibromatosis.
The most common presenting feature is painless mass (occasionally it may be
painful), other symptoms are caused by displacement or obstruction of normal
structures. Treatment is based on the primary tumor location and disease stage
which includes chemotherapy and surgery. Completely resected tumors have the