Moya Moya Disease:
It is a rare, progressive cerebrovascular disorder characterized by the narrowing
or occlusion of major blood vessels leading into the brain, and the formation
of abnormal blood vessels called moyamoya vessels. (ie "puff of smoke")
characterizes the appearance on angiography of abnormal vascular collateral
networks that develop adjacent to the stenotic vessels. The steno-occlusive
areas are usually bilateral, but unilateral involvement does not exclude the
diagnosis. Cerebral angiography in this case has shown poorly opacified intracranial
internal carotid artery and its branches. The CT Scan shows multiple infarcts
in bilateral cerebral hemisphere new and old.