Biliary atresia

The most common form is the absence of entire extrahepatic biliary tree at or above the porta hepatis. This results in the absence of bile in the stool that typically results in raised conjugated bilirubin and clay coloured stool. It is essential to differentiate this condition from Idiopathic Neonatal Hepatitis. Hepatobiliary scintigraphy using imidodicetic acid analogs is helpful to differentiate these two conditions. This scintigraphy shows good intake in liver but no excretion in the intestine.